Intern Med. 2019 Jun 7. doi: 10.2169/internalmedicine.2413-18. [Epub ahead of print]
Fatal Acute Exacerbation of Familial Interstitial Pneumonia Complicated with Dyskeratosis Congenita after Influenza Virus B Infection.

Tachiwada T1, Oda K1, Tahara M1, Sennari K1, Nemoto K1, Noguchi S1, Kawanami T1, Kido T1, Yamaguchi H2, Yatera K1.
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Dyskeratosis congenita (DC) is occasionally complicated in patients with familial interstitial pneumonia (FIP). However, there have been no reports of FIP patients with DC that develop acute exacerbation (AE). We herein report a FIP patient with DC that showed AE of FIP after influenza virus B infection. Although DC is a rare disease in clinical practice, physicians should keep in mind that FIP combined with DC has the potential to cause AE.


acute exacerbation; dyskeratosis congenita; familial interstitial pneumonia

PMID: 31178485 DOI: 10.2169/internalmedicine.2413-18
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